Expansion Cranioplasty with Jackscrew Distracters for Craniosynostosis and Intracranial Hypertension in Transplanted OsteopetrosisDowlati D. · Winston K.R. · Ketch L.L. · Quinones R. · Giller R. · Frattini A. · van Hove J.
Departments of aNeurosurgery and bPediatrics, The University of Colorado Health Sciences Center and The Children’s Hospital, Denver, Colo., USA; cDepartment of Human Genome, Institute of Biomedical Technologies, CNR, Segrate, Milan, Italy
Background: An 11-month-old boy with autosomal recessive infantile osteopetrosis presented, 7 months after bone marrow transplantation, with normal ventricular size and life-threatening intracranial hypertension due to pansynostosis. Methods: The cranial vault was expanded by using jackscrew distracters to upwardly advance the upper part of the calvarium. Results: The procedure achieved a 15-mm upward expansion of the cranial vault over a 15-day period, and the volume of the cranial vault was increased by 139 ml. All clinical manifestations of intracranial hypertension resolved. Conclusion: Cranial vault expansion with jackscrew distracters was successful in relieving intracranial hypertension in an infant with pancraniosynostosis complicating bone marrow transplanted malignant infantile osteopetrosis.
Ken R. Winston, MD
1056 East 19th Avenue, B330
Denver, CO 80218 (USA)
Tel. +1 303 861 6100, Fax +1 303 861 6101
Received: April 18, 2006
Accepted after revision: October 1, 2006
Number of Print Pages : 5
Number of Figures : 2, Number of Tables : 0, Number of References : 28
Vol. 43, No. 2, Year 2007 (Cover Date: February 2007)
Journal Editor: Frim, D.M. (Chicago, Ill.)
ISSN: 1016–2291 (print), 1423–0305 (Online)
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