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Vol. 110, No. 4, 2008
Issue release date: June 2008

Pulmonary Artery Aneurysm as a Cause for Chest Pain in a Patient with Noonan’s Syndrome: A Case Report

Brown J.R. · Plotnick G.
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Abstract

A pulmonary artery aneurysm is defined as pulmonary artery dilatation >4 cm. Pulmonary artery aneurysms are rare findings and are usually not associated with chest pain. This is the first report of a case of pulmonary artery aneurysm causing chest pain in a patient with Noonan’s syndrome. Chest X-ray showed cardiomegaly and a prominent main pulmonary artery segment and CT confirmed a pulmonary artery aneurysm with a pulmonary artery root measuring 5.6 cm. The patient underwent pulmonary valvuloplasty as well as pulmonary arterioplasty to repair the pulmonary artery aneurysm, and experienced subsequent relief of chest pain. In conclusion, pulmonary artery aneurysm is a rare complication in patients with Noonan’s syndrome and can be the cause of chest pain in such patients.



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Drug Dosage: The authors and the publisher have exerted every effort to ensure that drug selection and dosage set forth in this text are in accord with current recommendations and practice at the time of publication. However, in view of ongoing research, changes in goverment regulations, and the constant flow of information relating to drug therapy and drug reactions, the reader is urged to check the package insert for each drug for any changes in indications and dosage and for added warnings and precautions. This is particularly important when the recommended agent is a new and/or infrequently employed drug.
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References

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  2. Loukas M, Dabrowski M, Kantoch M, Ruzyłło W, Waltenberger J, Giannikopoulos P: A case report of Noonan’s syndrome with pulmonary valvar stenosis and coronary aneurysms. Med Sci Monit 2004;10:CS80–CS83.
  3. Purnell R, Williams I, Von Oppell U, Wood A: Giant aneurysms of the sinuses of Valsalva and aortic regurgitation in a patient with Noonan’s syndrome. Eur J Cardiothorac Surg 2005;28:346–348.
  4. Tami LF, McElderry MW: Pulmonary artery aneurysm due to severe congenital pulmonic stenosis: case report and literature review. Angiology 1994;45:383–390.
  5. Chetty KG, McGovern J, Mahutte CK: Hilar mass in a patient with chest pain. Chest 1996;109:1643–1644.
  6. Tindall H, Tandon AP, Ionescu MI: An unusual case of chest pain and cardiomegaly. Br J Clin Pract 1990;44:766–767.


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