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Table of Contents
Vol. 68, No. 2, 2010
Issue release date: June 2010
Section title: Paper
Free Access
Ann Nestlé [Engl] 2010;68:58–69
(DOI:10.1159/000312813)

Nutritional Management of Phenylketonuria

MacLeod E.L. · Ney D.M.
Department of Nutritional Sciences, University of Wisconsin, Madison, Wisc., USA
email Corresponding Author

Denise M. Ney

Department of Nutritional Sciences

University of Wisconsin

1415 Linden Drive, Madison, WI 53706 (USA)

Tel. +1 608 262 4386, Fax +1 608 262 5860, E-Mail ney@nutrisci.wisc.edu


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    External Resources
  68. Ney DM, Gleason ST, van Calcar SC, et al: Nutritional management of PKU with glycomacropeptide from cheese whey. J Inherit Metab Dis 2009;32:32–39.
  69. Sanjurjo P, Aldamiz L, Georgi G, et al: Dietary threonine reduces plasma phenylalanine levels in patients with hyperphenylalaninemia. J Pediatr Gastroenterol Nutr 2003;36:23–26.
  70. van Spronsen FJ, Burgard P: The truth of treating patients with phenylketonuria after childhood: the need for a new guideline. J Inherit Metab Dis 2008;31:673–679.