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Vol. 46, No. 1, 2010
Issue release date: June 2010
Pediatr Neurosurg 2010;46:54–57

Factor X Deficiency Presenting with Bilateral Chronic Subdural Hematoma

Senturk S. · Guzel E. · Hasanefendioglu Bayrak A. · Bukte Y. · Guzel A.
Departments of aRadiology and bNeurosurgery, Medical School, Dicle University, and cDepartment of Radiology, Veni Vidi Hospital, Diyarbakir, Turkey

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Factor X deficiency is a rare coagulation defect that can result in several hemorrhagic manifestations including central nervous system hematomas in infants and children. In this case report, we present computed tomography (CT) and magnetic resonance (MR) imaging findings of bilateral chronic subdural hematomas due to factor X deficiency. Cranial CT and MR imaging in a hypoactive 7-month-old male infant with right hemiparesis revealed bilateral chronic subdural hematomas at different stages. Laboratory findings showed a severe factor X deficiency, with a level of 0.7%. After fresh frozen plasma replacement, the patient was operated and the large hematoma on the left side evacuated. The patient recovered uneventfully and remained asymptomatic during the 1-year follow-up.

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    External Resources

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