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Case Series and Brief Reports

Free Access

Primary Orbital Cystic Pilocytic Astrocytoma

Mudhar H.S.a · Nuruddin M.b · Roy S.b

Author affiliations

aNational Specialist Ophthalmic Pathology Service (NSOPS), Department of Histopathology, Royal Hallamshire Hospital, Sheffield, UK; bChittagong Eye Infirmary and Training Complex, Chittagong, Bangladesh

Corresponding Author

Dr. Hardeep Singh Mudhar

National Specialist Ophthalmic Pathology Service (NSOPS)

Department of Histopathology, Royal Hallamshire Hospital

Glossop Road, Sheffield S10 2JF (UK)

E-Mail hardeep.mudhar@sth.nhs.uk

Related Articles for ""

Ocul Oncol Pathol 2016;2:280-284

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Abstract

Purpose: To describe the clinical, radiological and histopathological features of a highly unusual primary orbital glioma. Procedures: A 6-year-old female presented with right-sided proptosis that revealed a well-defined intraconal mass on CT imaging with intact orbital bony walls. During the removal of the lesion, it dissected away freely from the muscles and was separated from the optic nerve and globe. There was no communication with the brain. Results: Histology showed histological features highly favouring a pilocytic astrocytoma enveloped by meninges. No non-neoplastic brain tissue was identified. Conclusion: This is the first documentation of a primary orbital pilocytic astrocytoma not anatomically connected with the brain. We speculate that the tumour had arisen from developmental brain heterotopia.

© 2016 S. Karger AG, Basel


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Article / Publication Details

First-Page Preview
Abstract of Case Series and Brief Reports

Received: January 13, 2016
Accepted: June 23, 2016
Published online: July 20, 2016
Issue release date: October 2016

Number of Print Pages: 5
Number of Figures: 2
Number of Tables: 0

ISSN: 2296-4681 (Print)
eISSN: 2296-4657 (Online)

For additional information: https://www.karger.com/OOP


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